LMNA-risk VTA calculator

Risk Prediction Score for Life-Threatening Ventricular Tachyarrhythmias in Laminopathies

Sex
Non-missense LMNA mutation
Non-missense mutations include insertions, deletions, truncating mutations or mutations affecting splicing
Atrio-ventricular block
Please select the highest degree. 1st degree AV block corresponds to ≥0.20 sec PR interval and high degree AV block to type II 2nd degree or 3rd degree (and not type I 2nd degree)
Non-sustained ventricular tachycardia
NSVT corresponds to ≥3 consecutive ventricular complexes at a rate ≥120 bpm on 24-h ambulatory electrocardiographic monitoring
%
Left ventricular ejection fraction measurement derived from echocardiogram
Risk of Life-Threatening Ventricular Tachyarrhythmias at 5 years

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Life-Threatening Ventricular Tachyarrhythmias is defined as 1) sudden cardiac death, 2) appropriate ICD therapy, defined as a shock to terminate a VTA, or 3) other manifestations of hemodynamically unstable VTA